Rabbit Anti-Human BLOC1S6 pAb
-
产品编号
PA13781
-
别名
BLOC1S6, BLOS6, HPS9, PA, PALLID, PLDN
-
规格
- 50ul
- 100ul
Alias | BLOC1S6, BLOS6, HPS9, PA, PALLID, PLDN |
Catalog Number | PA13781 |
Molecular Name | BLOC1S6 |
Host | Rabbit |
Size | 50ul, 100ul |
Clonity | Polyclonal |
Purification | Affinity Purification |
Formulation | Supply in PBS with 0.02% sodium azide, 50% glycerol, pH 7.4. |
Immunogen | Recombinant fusion protein containing a sequence corresponding to a.a. 1-170 of human BLOC1S6 (NP_036520.1). |
Application | WB |
Storage Condition | Store the product under sterile conditions after opening at -20℃. Avoid freeze-thaw cycles. |
Shipping Condition | Shipped on ice packs. |
Product Declaration | 本产品仅用于研究用途(RUO)。不能用于诊断或直接用于人体实验。 |
Product Full Name | Rabbit Anti-Human BLOC1S6 Polyclonal Antibody |
BLOC1S6(溶酶体相关细胞器生物发生复合体亚基6)调控黑色素体形成,其突变导致Hermansky-Pudlak综合征(HPS8型),表现为眼皮肤白化病及肺纤维化。
可以,推荐使用黑色素瘤细胞或HPS患者皮肤活检,通过电镜观察黑色素体结构异常。
分装后-20℃保存,WB建议1:1000,IF建议1:200,有效期2年。