Rabbit Anti-Human DPF1 pAb
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产品编号
PA15630
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别名
DPF1, BAF45b, NEUD4, neuro-d4
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规格
- 50ul
- 100ul
Alias | DPF1, BAF45b, NEUD4, neuro-d4 |
Catalog Number | PA15630 |
Molecular Name | DPF1 |
Host | Rabbit |
Size | 50ul, 100ul |
Clonity | Polyclonal |
Purification | Affinity Purification |
Formulation | Supply in PBS with 0.02% sodium azide, 50% glycerol, pH 7.4. |
Immunogen | Recombinant fusion protein containing a sequence corresponding to a.a. 295-414 of human DPF1 (NP_001128627.1). |
Application | WB, IF |
Storage Condition | Store the product under sterile conditions after opening at -20℃. Avoid freeze-thaw cycles. |
Shipping Condition | Shipped on ice packs. |
Product Declaration | 本产品仅用于研究用途(RUO)。不能用于诊断或直接用于人体实验。 |
Product Full Name | Rabbit Anti-Human DPF1 Polyclonal Antibody |
ADAMTSL4(ADAMTS-like 4)调控细胞外基质组装,其突变导致先天性晶状体异位及马凡综合征样表型。
是的,推荐晶状体石蜡切片(柠檬酸修复pH 6.0),抗体稀释1:200;WB预期条带约120 kDa。
与人ADAMTSL4同源性约75%,需预实验验证(推荐WB起始稀释1:500)。
提供先天性晶状体异位患者样本的WB阴性对照数据。
是的,提供患者皮肤成纤维细胞中ADAMTSL4表达缺失的IHC结果。