Rabbit Anti-Human BBOX1 pAb
-
产品编号
PA14378
-
别名
BBOX1, BBH, BBOX, G-BBH, gamma-BBH
-
规格
- 50ul
- 100ul
| Catalog Number | PA14378 |
| Alias | BBOX1, BBH, BBOX, G-BBH, gamma-BBH |
| Size | 50ul, 100ul |
| Product Full Name | Rabbit Anti-Human BBOX1 Polyclonal Antibody |
| Molecular Name | BBOX1 |
| Host | Rabbit |
| Clonity | Polyclonal |
| Purification | Affinity Purification |
| Storage Condition | Store the product under sterile conditions after opening at -20℃. Avoid freeze-thaw cycles. |
| Formulation | Supply in PBS with 0.02% sodium azide, 50% glycerol, pH 7.4. |
| Shipping Condition | Shipped on ice packs. |
| Immunogen | Recombinant fusion protein containing a sequence corresponding to a.a. 1-180 of human BBOX1 (NP_003977.1). |
| Application | WB |
| Product Declaration | 本产品仅用于研究用途(RUO)。不能用于诊断或直接用于人体实验。 |
BBOX1(γ-丁酰甜菜碱羟化酶)催化肉碱合成,调控脂肪酸氧化及能量代谢,其缺陷导致肉碱缺乏症及心肌病。
可以,推荐使用肉碱耗竭模型,通过质谱检测肉碱及其前体水平变化。
经测试无交叉反应,特异性针对BBOX1。
0